CHARACTERISTICS OF CYSTIC FIBROSIS IN THE KRASNODAR REGION ACCORDING TO A EUROPEAN REGISTER FOR 2011

Creation of the Russian register of patients with cystic fibrosis and participation in the program European register is essential for patients in the region and in the country. Result of creating and analyzing annual data register should be the understanding of the following fundamental epidemiological indicators: number of patients, including deaths, number, patient age, their sex distribution. Analysis of the register of patients showed that the proportion of children and adolescents dominates adults (58 children and 14 adults), the average age of the patients below the other regions of the country and the world. Clinical-laboratory features of cystic fibrosis in the Krasnodar region showed an increase in complications of the disease and Pseudomonas aeruginosa infection with age. Total number of mutations have been identified 7, which was 75%. Results register landmark adoption of adequate institutional, medical and social measures when working with patients suffering from cystic fibrosis.